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首頁(yè) > 抗體 > 一抗 > 其它 > Mannose Phosphate Isomerase mouse mAb
Mannose Phosphate Isomerase mouse mAb
商品貨號(hào): PLA005196
適 應(yīng) 性: 人,大鼠
WB ICC
¥600元
規(guī)格:
在線咨詢
MSDS
說(shuō)明書
商品描述
  • 發(fā)貨日期: 7
  • 基因名稱: mpi
  • Human_gene_id: 4351
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=4351
  • Human_swiss_prot_no: P34949
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/P34949/entry
  • Mouse_swiss_prot_no: Q924M7
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/Q924M7
  • 特異性: This antibody detects endogenous levels of Mannose Phosphate Isomerase and does not cross-react with related proteins.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來(lái)源: Monoclonal, Mouse
  • 稀釋: wb 1:1000 icc 1:300
  • 純化工藝: The antibody was affinity-purified from mouse ascites by affinity-chromatography using epitope-specific immunogen.
  • 濃度: 1 mg/ml
  • 儲(chǔ)存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說(shuō)明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: PMI1;CDG1B;FLJ39201;Mannose 6 phosphate isomerase;Mannose-6-phosphate isomerase; MANNOSEPHOSPHATE ISOMERASE;MGC94106;MPI;MPI_HUMAN;Phosphohexomutase;phosphomannose isomerase 1;Phosphomannose isomerase;PMI;PMI1.
  • 實(shí)測(cè)條帶: 54kD
  • 信號(hào)通路: Fructose and mannose metabolism;Amino sugar and nucleotide sugar metabolism;
  • 功能: catalytic activity:D-mannose 6-phosphate = D-fructose 6-phosphate.,cofactor:Binds 1 zinc ion per subunit.,disease:Defects in MPI are the cause of congenital disorder of glycosylation type 1B (CDG1B) [MIM:602579]; also known as carbohydrate-deficient glycoprotein syndrome type Ib (CDGS1B). Congenital disorders of glycosylation are metabolic deficiencies in glycoprotein biosynthesis that usually cause severe mental and psychomotor retardation. They are characterized by under-glycosylated serum glycoproteins. CDG1B is clinically characterized by protein-losing enteropathy.,function:Involved in the synthesis of the GDP-mannose and dolichol-phosphate-mannose required for a number of critical mannosyl transfer reactions.,pathway:Nucleotide-sugar biosynthesis; GDP-D-mannose biosynthesis; alpha-D-mannose 1-phosphate from D-fructose 6-phosphate: step 1/2.,similarity:Belongs to the mannose-6-phosphate isomerase type 1 family.,tissue specificity:Expressed in all tissues, but more abundant in heart, brain and skeletal muscle.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細(xì)胞定位: Cytoplasm .
  • 組織表達(dá): Expressed in all tissues, but more abundant in heart, brain and skeletal muscle.
  • 科研貨號(hào): PLA005196
Mannose Phosphate Isomerase mouse mAb
Catalog No PLA005196
Product information
  • 發(fā)貨日期: 7
  • 基因名稱: mpi
  • Human_gene_id: 4351
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=4351
  • Human_swiss_prot_no: P34949
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/P34949/entry
  • Mouse_swiss_prot_no: Q924M7
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/Q924M7
  • 特異性: This antibody detects endogenous levels of Mannose Phosphate Isomerase and does not cross-react with related proteins.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來(lái)源: Monoclonal, Mouse
  • 稀釋: wb 1:1000 icc 1:300
  • 純化工藝: The antibody was affinity-purified from mouse ascites by affinity-chromatography using epitope-specific immunogen.
  • 濃度: 1 mg/ml
  • 儲(chǔ)存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說(shuō)明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: PMI1;CDG1B;FLJ39201;Mannose 6 phosphate isomerase;Mannose-6-phosphate isomerase; MANNOSEPHOSPHATE ISOMERASE;MGC94106;MPI;MPI_HUMAN;Phosphohexomutase;phosphomannose isomerase 1;Phosphomannose isomerase;PMI;PMI1.
  • 實(shí)測(cè)條帶: 54kD
  • 信號(hào)通路: Fructose and mannose metabolism;Amino sugar and nucleotide sugar metabolism;
  • 功能: catalytic activity:D-mannose 6-phosphate = D-fructose 6-phosphate.,cofactor:Binds 1 zinc ion per subunit.,disease:Defects in MPI are the cause of congenital disorder of glycosylation type 1B (CDG1B) [MIM:602579]; also known as carbohydrate-deficient glycoprotein syndrome type Ib (CDGS1B). Congenital disorders of glycosylation are metabolic deficiencies in glycoprotein biosynthesis that usually cause severe mental and psychomotor retardation. They are characterized by under-glycosylated serum glycoproteins. CDG1B is clinically characterized by protein-losing enteropathy.,function:Involved in the synthesis of the GDP-mannose and dolichol-phosphate-mannose required for a number of critical mannosyl transfer reactions.,pathway:Nucleotide-sugar biosynthesis; GDP-D-mannose biosynthesis; alpha-D-mannose 1-phosphate from D-fructose 6-phosphate: step 1/2.,similarity:Belongs to the mannose-6-phosphate isomerase type 1 family.,tissue specificity:Expressed in all tissues, but more abundant in heart, brain and skeletal muscle.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細(xì)胞定位: Cytoplasm .
  • 組織表達(dá): Expressed in all tissues, but more abundant in heart, brain and skeletal muscle.
  • 科研貨號(hào): PLA005196
  • Hunan UPT Biotechnology Co.,Ltd
    Website:m.hyjdss.com Servive hotline :4006916686
    E-mail:service@uptbio.com
    Address:
    Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.
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