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PEPCK Monoclonal Antibody

商品貨號(hào)： PLA005135

適應(yīng) 性： 人,小鼠,大鼠,牛,狗,豬

￥600元

規(guī)格：

40μL 100μL 200μL

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MSDS

說(shuō)明書

商品描述

發(fā)貨日期： 7
基因名稱： PCK2
蛋白名稱： Phosphoenolpyruvate carboxykinase [GTP] mitochondrial
Human_gene_id： 5106
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=5106
Human_swiss_prot_no： Q16822
Human_swiss_link： http://www.uniprot.org/uniprotkb/Q16822/entry
Mouse_gene_id： 74551
Mouse_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=74551
Mouse_swiss_prot_no： Q8BH04
Mouse_swiss_link： http://www.uniprot.org/uniprot/Q8BH04
特異性： PEPCK Monoclonal Antibody detects endogenous levels of PEPCK protein.
組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
來(lái)源： Monoclonal, Mouse
稀釋： WB 1:1000 - 1:2000. Not yet tested in other applications.
純化工藝： Affinity purification
濃度： 1 mg/ml
儲(chǔ)存： -15°C to -25°C/1 year(Do not lower than -25°C)
說(shuō)明書： 1
Msds： MSDS_Antibody.pdf
其他名稱： PCK2; PEPCK2; Phosphoenolpyruvate carboxykinase [GTP]; mitochondrial; PEPCK-M; Phosphoenolpyruvate carboxylase
信號(hào)通路： Glycolysis / Gluconeogenesis;Citrate cycle (TCA cycle);Pyruvate metabolism;PPAR;Insulin_Receptor;Adipocytokine;
功能： catalytic activity:GTP + oxaloacetate = GDP + phosphoenolpyruvate + CO(2).,cofactor:Binds 1 manganese ion per subunit.,cofactor:Manganese.,disease:Defects in PCK2 are the cause of mitochondrial phosphoenolpyruvate carboxykinase deficiency (mitochondrial PEPCK deficiency) [MIM:261650]. PEPCK deficiency is a metabolic disorder resulting from impaired gluconeogenesis. It is a rare disease with less than 10 cases reported in the literature. Clinical characteristics include hypotonia, hepatomegaly, failure to thrive, lactic acidosis and hypoglycaemia. Autoposy reveals fatty infiltration of both the liver and kidneys. The disorder is transmitted as an autosomal recessive trait.,function:Catalyzes the conversion of oxaloacetate (OAA) to phosphoenolpyruvate (PEP), the rate-limiting step in the metabolic pathway that produces glucose from lactate and other precursors derived from the citric acid cycle.,miscellaneous:In eukaryotes there are two isozymes: a cytoplasmic one and a mitochondrial one.,pathway:Carbohydrate biosynthesis; gluconeogenesis.,PTM:Phosphorylated upon DNA damage, probably by ATM or ATR.,similarity:Belongs to the phosphoenolpyruvate carboxykinase [GTP] family.,subunit:Monomer.,
相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
細(xì)胞定位： Mitochondrion.
組織表達(dá)： Liver,Neuroblastoma,Placenta,
tag： hot
科研貨號(hào)： PLA005135

PEPCK Monoclonal Antibody

Catalog No PLA005135

Product information

發(fā)貨日期： 7
基因名稱： PCK2
蛋白名稱： Phosphoenolpyruvate carboxykinase [GTP] mitochondrial
Human_gene_id： 5106
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=5106
Human_swiss_prot_no： Q16822
Human_swiss_link： http://www.uniprot.org/uniprotkb/Q16822/entry
Mouse_gene_id： 74551
Mouse_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=74551
Mouse_swiss_prot_no： Q8BH04
Mouse_swiss_link： http://www.uniprot.org/uniprot/Q8BH04
特異性： PEPCK Monoclonal Antibody detects endogenous levels of PEPCK protein.
組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
來(lái)源： Monoclonal, Mouse
稀釋： WB 1:1000 - 1:2000. Not yet tested in other applications.
純化工藝： Affinity purification
濃度： 1 mg/ml
儲(chǔ)存： -15°C to -25°C/1 year(Do not lower than -25°C)
說(shuō)明書： 1
Msds： MSDS_Antibody.pdf
其他名稱： PCK2; PEPCK2; Phosphoenolpyruvate carboxykinase [GTP]; mitochondrial; PEPCK-M; Phosphoenolpyruvate carboxylase
信號(hào)通路： Glycolysis / Gluconeogenesis;Citrate cycle (TCA cycle);Pyruvate metabolism;PPAR;Insulin_Receptor;Adipocytokine;
功能： catalytic activity:GTP + oxaloacetate = GDP + phosphoenolpyruvate + CO(2).,cofactor:Binds 1 manganese ion per subunit.,cofactor:Manganese.,disease:Defects in PCK2 are the cause of mitochondrial phosphoenolpyruvate carboxykinase deficiency (mitochondrial PEPCK deficiency) [MIM:261650]. PEPCK deficiency is a metabolic disorder resulting from impaired gluconeogenesis. It is a rare disease with less than 10 cases reported in the literature. Clinical characteristics include hypotonia, hepatomegaly, failure to thrive, lactic acidosis and hypoglycaemia. Autoposy reveals fatty infiltration of both the liver and kidneys. The disorder is transmitted as an autosomal recessive trait.,function:Catalyzes the conversion of oxaloacetate (OAA) to phosphoenolpyruvate (PEP), the rate-limiting step in the metabolic pathway that produces glucose from lactate and other precursors derived from the citric acid cycle.,miscellaneous:In eukaryotes there are two isozymes: a cytoplasmic one and a mitochondrial one.,pathway:Carbohydrate biosynthesis; gluconeogenesis.,PTM:Phosphorylated upon DNA damage, probably by ATM or ATR.,similarity:Belongs to the phosphoenolpyruvate carboxykinase [GTP] family.,subunit:Monomer.,
相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
細(xì)胞定位： Mitochondrion.
組織表達(dá)： Liver,Neuroblastoma,Placenta,
tag： hot
科研貨號(hào)： PLA005135

Hunan UPT Biotechnology Co.,Ltd

Website：m.hyjdss.com Servive hotline :4006916686

E-mail：service@uptbio.com

Address：

Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.