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MYL2 Monoclonal Antibody
商品貨號: PLA004945
適 應(yīng) 性:
WB ELISA
¥600元
規(guī)格:
在線咨詢
MSDS
說明書
商品描述
  • 發(fā)貨日期: 7
  • 基因名稱: MYL2
  • 蛋白名稱: Myosin regulatory light chain 2 ventricular/cardiac muscle isoform
  • Human_gene_id: 4633
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=4633
  • Human_swiss_prot_no: P10916
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/P10916/entry
  • Mouse_swiss_prot_no: P51667
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/P51667
  • 特異性: MYL2 Monoclonal Antibody detects endogenous levels of MYL2 protein.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源: Monoclonal, Mouse
  • 稀釋: WB 1:500 - 1:2000. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝: Affinity purification
  • 儲存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: MYL2; Myosin regulatory light chain 2; ventricular/cardiac muscle isoform; MLC-2; MLC-2v
  • 信號通路: Cardiac muscle contraction;Focal adhesion;Tight junction;Leukocyte transendothelial migration;Regulates Actin and Cytoskeleton;Hypertrophic cardiomyopathy (HCM);Dilated cardiomyopathy;
  • 功能: disease:Defects in MYL2 are the cause of cardiomyopathy familial hypertrophic type 10 (CMH10) [MIM:608758]. Familial hypertrophic cardiomyopathy is a hereditary heart disorder characterized by ventricular hypertrophy, which is usually asymmetric and often involves the interventricular septum. The symptoms include dyspnea, syncope, collapse, palpitations, and chest pain. They can be readily provoked by exercise. The disorder has inter- and intrafamilial variability ranging from benign to malignant forms with high risk of cardiac failure and sudden cardiac death.,disease:Defects in MYL2 are the cause of cardiomyopathy hypertrophic with mid-left ventricular chamber type 2 (MVC2) [MIM:608758]. MVC2 is a very rare variant of familial hypertrophic cardiomyopathy, characterized by mid-left ventricular chamber thickening.,miscellaneous:This chain binds calcium.,similarity:Contains 3 EF-hand domains.,subunit:Myosin is an hexamer of 2 heavy chains and 4 light chains.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細胞定位: Cytoplasm, myofibril, sarcomere, A band .
  • 組織表達: Highly expressed in type I muscle fibers.
  • 科研貨號: PLA004945
MYL2 Monoclonal Antibody
Catalog No PLA004945
Product information
  • 發(fā)貨日期: 7
  • 基因名稱: MYL2
  • 蛋白名稱: Myosin regulatory light chain 2 ventricular/cardiac muscle isoform
  • Human_gene_id: 4633
  • Human_gene_link: http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=4633
  • Human_swiss_prot_no: P10916
  • Human_swiss_link: http://www.uniprot.org/uniprotkb/P10916/entry
  • Mouse_swiss_prot_no: P51667
  • Mouse_swiss_link: http://www.uniprot.org/uniprot/P51667
  • 特異性: MYL2 Monoclonal Antibody detects endogenous levels of MYL2 protein.
  • 組成: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來源: Monoclonal, Mouse
  • 稀釋: WB 1:500 - 1:2000. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝: Affinity purification
  • 儲存: -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說明書: 1
  • Msds: MSDS_Antibody.pdf
  • 其他名稱: MYL2; Myosin regulatory light chain 2; ventricular/cardiac muscle isoform; MLC-2; MLC-2v
  • 信號通路: Cardiac muscle contraction;Focal adhesion;Tight junction;Leukocyte transendothelial migration;Regulates Actin and Cytoskeleton;Hypertrophic cardiomyopathy (HCM);Dilated cardiomyopathy;
  • 功能: disease:Defects in MYL2 are the cause of cardiomyopathy familial hypertrophic type 10 (CMH10) [MIM:608758]. Familial hypertrophic cardiomyopathy is a hereditary heart disorder characterized by ventricular hypertrophy, which is usually asymmetric and often involves the interventricular septum. The symptoms include dyspnea, syncope, collapse, palpitations, and chest pain. They can be readily provoked by exercise. The disorder has inter- and intrafamilial variability ranging from benign to malignant forms with high risk of cardiac failure and sudden cardiac death.,disease:Defects in MYL2 are the cause of cardiomyopathy hypertrophic with mid-left ventricular chamber type 2 (MVC2) [MIM:608758]. MVC2 is a very rare variant of familial hypertrophic cardiomyopathy, characterized by mid-left ventricular chamber thickening.,miscellaneous:This chain binds calcium.,similarity:Contains 3 EF-hand domains.,subunit:Myosin is an hexamer of 2 heavy chains and 4 light chains.,
  • 相關(guān)產(chǎn)品: RS0001,RS0002,YM3028,YM3029
  • 細胞定位: Cytoplasm, myofibril, sarcomere, A band .
  • 組織表達: Highly expressed in type I muscle fibers.
  • 科研貨號: PLA004945
  • Hunan UPT Biotechnology Co.,Ltd
    Website:m.hyjdss.com Servive hotline :4006916686
    E-mail:service@uptbio.com
    Address:
    Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.
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