日韩伦片在线视频,激情综合网激情六月,天天操天天添天天日天天干

<ul id="0mk2q"></ul>

> > > >

HPS-1 Monoclonal Antibody

商品貨號： PLA004852

適應(yīng) 性： 人

￥600元

規(guī)格：

40μL 100μL 200μL

在線咨詢

MSDS

說明書

商品描述

發(fā)貨日期： 7
基因名稱： HPS1
蛋白名稱： Hermansky-Pudlak syndrome 1 protein
Human_gene_id： 3257
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=3257
Human_swiss_prot_no： Q92902
Human_swiss_link： http://www.uniprot.org/uniprotkb/Q92902/entry
Mouse_swiss_prot_no： O08983
Mouse_swiss_link： http://www.uniprot.org/uniprot/O08983
特異性： HPS-1 Monoclonal Antibody detects endogenous levels of HPS-1 protein.
組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
來源： Monoclonal, Mouse
稀釋： WB 1:500 - 1:2000. ELISA: 1:10000. Not yet tested in other applications.
純化工藝： Affinity purification
儲存： -15°C to -25°C/1 year(Do not lower than -25°C)
說明書： 1
Msds： MSDS_Antibody.pdf
其他名稱： HPS1; HPS; Hermansky-Pudlak syndrome 1 protein
功能： alternative products:Additional isoforms seem to exist,disease:Defects in HPS1 are the cause of Hermansky-Pudlak syndrome type 1 (HPS1) [MIM:203300]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.,function:Component of multiple cytoplasmic organelles. Apparently crucial for their normal development and function. May be involved in intracellular protein sorting.,online information:HPS1 mutations,online information:Retina International's Scientific Newsletter,tissue specificity:Ubiquitous.,
相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
細(xì)胞定位： cytoplasm,lysosome,integral component of plasma membrane,cytoplasmic, membrane-bounded vesicle,BLOC-3 complex,cytoplasmic vesicle,
組織表達(dá)： Ubiquitous.
科研貨號： PLA004852

HPS-1 Monoclonal Antibody

Catalog No PLA004852

Product information

發(fā)貨日期： 7
基因名稱： HPS1
蛋白名稱： Hermansky-Pudlak syndrome 1 protein
Human_gene_id： 3257
Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=3257
Human_swiss_prot_no： Q92902
Human_swiss_link： http://www.uniprot.org/uniprotkb/Q92902/entry
Mouse_swiss_prot_no： O08983
Mouse_swiss_link： http://www.uniprot.org/uniprot/O08983
特異性： HPS-1 Monoclonal Antibody detects endogenous levels of HPS-1 protein.
組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
來源： Monoclonal, Mouse
稀釋： WB 1:500 - 1:2000. ELISA: 1:10000. Not yet tested in other applications.
純化工藝： Affinity purification
儲存： -15°C to -25°C/1 year(Do not lower than -25°C)
說明書： 1
Msds： MSDS_Antibody.pdf
其他名稱： HPS1; HPS; Hermansky-Pudlak syndrome 1 protein
功能： alternative products:Additional isoforms seem to exist,disease:Defects in HPS1 are the cause of Hermansky-Pudlak syndrome type 1 (HPS1) [MIM:203300]. Hermansky-Pudlak syndrome (HPS) is a genetically heterogeneous, rare, autosomal recessive disorder characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.,function:Component of multiple cytoplasmic organelles. Apparently crucial for their normal development and function. May be involved in intracellular protein sorting.,online information:HPS1 mutations,online information:Retina International's Scientific Newsletter,tissue specificity:Ubiquitous.,
相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
細(xì)胞定位： cytoplasm,lysosome,integral component of plasma membrane,cytoplasmic, membrane-bounded vesicle,BLOC-3 complex,cytoplasmic vesicle,
組織表達(dá)： Ubiquitous.
科研貨號： PLA004852

Hunan UPT Biotechnology Co.,Ltd

Website：m.hyjdss.com Servive hotline :4006916686

E-mail：service@uptbio.com

Address：

Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.